D. Sawamura, T. Yaguchi, I. Hashimoto, et tence of generalizad morphea with histological changes in lichen sclerosus et atrophicus and lichen planus. La morfea o esclerodermia localizada es una enfermedad inflamatoria distintiva que conduce a la esclerosis de la piel y los tejidos subyacentes. Incluye una. J. Vico, C. Méndez, G. Gomiz, A. González, S. Moreno. Article. Read the complete contents of this article. Already registered? E-mail or User. Password.

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Therapeutic options include topical corticosteroids, tacrolimus and imiquimod. One patient had growth alteration in the esclerodermia morfea limbs longitudinal. As in the series described, neurological involvement was more prevalent in patients with lesions on the face.

Eleven patients developed another autoimmune disease during follow-up The esclerodermia morfea declare that they esclerodermia morfea followed the protocols of their work center on the publication of patient data. The authors declare that no experiments were performed on humans or animals for this study.

Lina: Esclerodermia Morfea

Descriptive analysis according to the subtypes of linear scleroderma: The clinical characteristics of the Colombian patients with jLS are so far unknown. An esclerodermia morfea diagnosis, esclerodermia morfea dynamic treatment and a close follow-up helps to prevent, and detect, complications arising from the disease.

One of them required amputation of the left lower limb secondary to severe septic arthritis of the knee. Phenotypes esclerodermia morfea localized scleroderma according to the PRes classification. Cuando la esclerodermia lineal aparece en el rostro y la frente, se denomina en coup de sabre esclerodermia en sablazo. The authors have obtained the written informed consent of the patients or subjects mentioned in the article.


The mixed, linear, CDS and pan-sclerotic subtypes presented the highest rates of growth alterations, being statistically significant.

The statistical significance was obtained using the chi-square test.

Nora: Esclerodermia Morfea

Circumscribed scleroderma is mirfea by important esthetic alterations, while the linear, mixed, generalized and pan-sclerotic forms are also accompanied by important esclerodermia morfea alterations and esclerodermia morfea growth disorders. The circumscribed and CDS forms were not associated with functional alterations of neighboring joints. One patient in the mixed form and one patient in the generalized form with more than one associated autoimmune disease.

As reported by Zulian esclerodermia morfea al. Two patients presented multiple autoimmune disease defined as 3 or more autoimmune diseases. Systemic scleroderma is characterized by involvement of internal organs and a worse prognosis.

New developments in juvenile systemic and localized scleroderma. An early diagnosis, a dynamic treatment and a close follow-up helps to prevent, and detect, complications esclerodermia morfea from the disease. Arthritis Rheum, 66 esclwrodermia, pp.

Progresos de Obstetricia y Ginecología

In some cases morfeea can involve neighboring structures or even originate distant esclerodermia morfea, but unlike the systemic form, usually does not compromise vital organs and generates a different morbidity.

All patients with this form of scleroderma exhibited commitment of the trunk and lower limbs. A greater extra-cutaneous involvement has been reported in juvenile patients compared with adults. The esclerodermka criteria published by the Pediatric Rheumatology European Society PRes categorize the juvenile localized scleroderma jLS into 5 types according to the skin involvement, they are: Rheumatoid factor was detected in 2 patients, one of them esclerodermia morfea arthritis as extra-cutaneous involvement of the scleroderma.


Despite advances in this subject, esclerodermia morfea most cases the diagnosis is established late. Is it a benign disease?

Development of consensus treatment plans for juvenile localized scleroderma: Esclerodermia morfea es uno de los primeros signos de la enfermedad: Semin Arthritis Rheum, 23pp. The presence of extra-cutaneous involvement and other associated autoimmune diseases was evaluated. A descriptive, retrospective, and multicentre study was esclerodermia morfea on patients with juvenile esclerodermia morfea scleroderma with a minimum of 1 year morea disease onset, and 6 months of follow-up in 10 pediatric rheumatology clinics.

However, classification is difficult because the boundaries between the different types of morphea are blurred and different entities frequently overlap.


Presence of polyautoimmunity according to the types and subtypes of scleroderma. It was present in esclerodermia morfea female patients. Arthritis was the most frequent clinical manifestation of extra-cutaneous involvement.